Megacystis-Microcolon-Intestinal Hypoperistalsis Syndrome (MMIHS).

Introduction Megacystismicrocolon -intestinal hypoperistalsis syndrome(MMIHS) also called as BERDON SYNDROME is a rare congenital disease characterized by massive abdominal distension caused by a largely dilated non-obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. It poses a diagnostic and therapeutic challenge to the surgeon. It the most severe form of functional intestinal obstruction in the newborn. Most patients with MMIHS are not able to void spontaneously. Long term prognosis is bad. We report you this rarity with a review of various aspect of disease.